| 54092-700 | Elaprase | Non-Proprietary Name: Idursulfase | Solution, Concentrate | Intravenous | Takeda Pharmaceuticals America, Inc. | ACTIVE |
| 58468-0040 | Fabrazyme | Non-Proprietary Name: Agalsidase Beta | Injection, Powder, Lyophilized, For Solution | Intravenous | Genzyme Corporation | ACTIVE |
| 58468-0041 | Fabrazyme | Non-Proprietary Name: Agalsidase Beta | Injection, Powder, Lyophilized, For Solution | Intravenous | Genzyme Corporation | ACTIVE |
| 58468-0070 | Aldurazyme | Non-Proprietary Name: Laronidase | Injection, Solution, Concentrate | Intravenous | Genzyme Corporation | ACTIVE |
| 58468-0160 | Lumizyme | Non-Proprietary Name: Alglucosidase Alfa | Injection, Powder, For Solution | Intravenous | Genzyme Corporation | ACTIVE |
| 58468-0426 | Nexviazyme ngpt | Non-Proprietary Name: Avalglucosidase Alfa | Injection, Powder, Lyophilized, For Solution | Intravenous | Genzyme Corporation | ACTIVE |
| 68135-020 | | Non-Proprietary Name: Galsulfase | Solution | | Biomarin Pharmaceutical Inc. | ACTIVE |
| 68135-020 | Naglazyme | Non-Proprietary Name: Galsulfase | Solution | Intravenous | Biomarin Pharmaceutical Inc. | ACTIVE |
| 68135-100 | | Non-Proprietary Name: Elosulfase Alfa | Injection, Solution, Concentrate | | Biomarin Pharmaceutical Inc. | ACTIVE |
| 68135-100 | Vimizim | Non-Proprietary Name: Elosulfase Alfa | Injection, Solution, Concentrate | Intravenous | Biomarin Pharmaceutical Inc. | ACTIVE |